Dermatofibrosarcoma Protuberans- A Case Report

Abstract

Dermatofibrosarcoma Protuberans (DFSP) is an uncommon soft tissue tumor that involves the dermis, subcutaneous fat, and in rare cases, muscle and fascia. It represents less than 0.1% of all tumors, but is considered to be the most common skin sarcoma. We present one such case where histopathology and immunohistochemistry helped clinch the diagnosis .DFSP has a high rate of recurrence but a low rate of metastasis. Wide surgical excision is the cornerstone of treatment for DFSP.