Abstract

新生児の内科治療に反応しない重篤な低血糖の原因として,稀ではあるが,膵島細胞症が知られている.我々は緊急帝王切開で出生後,持続性高インスリン血症性低血糖症を呈し,心不全と感染症を併発,死亡後,膵局所の剖検が行われた症例を経験した.病理組織学的には ductulo-insular complex 像を呈していた.このような経過をとる症例の病態機序を明らかにし,治療を考える上で重要であると考え報告する.

Keywords:
Nesidioblastosis Medicine Autopsy General surgery Pancreas Pediatrics Internal medicine

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Topics

Cardiovascular Function and Risk Factors
Health Sciences →  Medicine →  Cardiology and Cardiovascular Medicine
Cardiac electrophysiology and arrhythmias
Health Sciences →  Medicine →  Cardiology and Cardiovascular Medicine
Hyperglycemia and glycemic control in critically ill and hospitalized patients
Health Sciences →  Medicine →  Endocrinology, Diabetes and Metabolism

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